Noncompaction cardiomyopathy: A rare cardiomyopathy

Introduction: Noncompaction cardiomyopathy (NccM) is a rare form of cardiomyopathy. the American Heart Association classified it as a genetic cardiomyopathy. the pathogenesis of this condition is attributed to the failure of trabecular myocardium to compact and underdeveloped microcoronary circulation. case report: We present a case of a 72-year-old African American female who presented with shortness of breath and leg swelling and was found to have severe systolic dysfunction. stress test showed ischemia. Left heart catheterization which included left ventriculogram showed prominent trabeculations suggestive of noncompaction cardiomyopathy. conclusion: this condition is often associated with other congenital cardiac defects and arrthymias. When it is present alone, it is called isolated noncompaction cardiomyopathy (INccM). the treatment protocol for this cardiomyopathy is the same as other cardiomyopathies, and includes the management of arrhythmias, heart failure and potential risk of embolism.